Thrombotic thrombocytopenic purpura (TTP) is a rare, life threatened disease. It is characterized by fever, variable neurological manifestations, progressive renal failure, microangiopathic hemolytic anemia and thrombocytopenia.
TTP may be associated with some autoimmune diseases such as systemic lupus erythematosus (SLE). TTP may be confused with SLE because its classical sympoms such as fever, neurological manifestations, renal failure, thrombocytopenia can be seen in SLE.
We report here a patient with TTP, confused with SLE, and whom the diagnosis of TTP was supported by autopsi.